Momen M A, Haque M M, Akhter S, Ahmed M, Rabbani M G, Rahman N
Department of Surgery, Rajshahi Medical College, Rajshahi, Bangladesh.
Mymensingh Med J. 2011 Jul;20(3):493-6.
Penile agenesis (PA) is an extremely rare congenital anomaly with profound surgical and psychosocial consequences. Only seventy five cases have been reported in the literature, the highest age of presentation known seven years. We present a twenty six years old otherwise normal aphallic male with attraction to female sex and night emission through anus. The patient did not agree to the female gender assignment and functioning phallic reconstruction is practically unavailable. Early female gender assignment and feminizing perineal reconstruction (Vaginoplasty) in neonatal cases is the technically easier goal of treatment. Late presenting cases add difficulty to debated decision making of gender assignment.
阴茎发育不全(PA)是一种极其罕见的先天性异常,会带来严重的手术和心理社会后果。文献中仅报道了75例病例,已知的最高发病年龄为7岁。我们报告了一名26岁的男性,除阴茎缺失外身体其他方面正常,有对女性的性吸引力且通过肛门遗精。该患者不同意进行女性性别认定,而且实际上无法进行功能性阴茎重建。在新生儿病例中尽早进行女性性别认定和女性化会阴重建(阴道成形术)在技术上是更容易实现的治疗目标。发病较晚的病例给性别认定这一存在争议的决策增加了难度。