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表现为反复不明原因晕厥的肥厚型心肌病。

Apical hypertrophic cardiomyopathy presenting as recurrent unexplained syncope.

作者信息

Kasirye Yusuf, Manne Janaki Ram, Epperla Narendranath, Bapani Sowjanya, Garcia-Montilla Romel

机构信息

Department of Internal Medicine, Marshfield Clinic, 50 Sherry Avenue, Park Falls, WI 54552, USA.

出版信息

Clin Med Res. 2012 Feb;10(1):26-31. doi: 10.3121/cmr.2011.986. Epub 2011 Aug 4.

DOI:10.3121/cmr.2011.986
PMID:21817119
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3280460/
Abstract

Apical hypertrophic cardiomyopathy (AHC) is a rare variant of hypertrophic cardiomyopathy. Since its description by Sakamoto in 1976 in Japanese patients, our understanding of this entity has evolved. Although cardiac magnetic resonance imaging has emerged as the gold standard for diagnosing AHC, clinical attention must be drawn to the unique electrocardiographic features that provide the initial clues to making the diagnosis. In this case, we present a 47-year-old man with AHC who presented with recurrent syncope, but anomalies on his electrocardiogram went unnoticed on two clinical encounters. He was subsequently admitted to our service and rapidly diagnosed after we observed the very classical findings in the plain twelve lead electrocardiogram done at the time of admission. In a clinical encounter involving a patient presenting with recurrent syncope, special attention must be focused on the electrocardiogram to decipher the unique diagnostic features it might show.

摘要

心尖肥厚型心肌病(AHC)是肥厚型心肌病的一种罕见变体。自1976年坂本在日本患者中对其进行描述以来,我们对这一病症的认识不断发展。尽管心脏磁共振成像已成为诊断AHC的金标准,但临床仍须关注那些为诊断提供初步线索的独特心电图特征。在此病例中,我们报告一名47岁患有AHC的男性,他反复出现晕厥,但在两次临床接诊时其心电图异常均未被注意到。随后他入住我院,在我们观察到入院时所做的普通十二导联心电图上的典型表现后,迅速得以确诊。在涉及反复晕厥患者的临床接诊中,必须特别关注心电图,以解读其可能显示的独特诊断特征。

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Myocardial perfusion SPECT in the diagnosis of apical hypertrophic cardiomyopathy.心肌灌注单光子发射计算机断层扫描在诊断心尖肥厚型心肌病中的应用
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