Volney Giselle, Wada Habiba, Tatusov Michael
Internal Medicine, Ross University School of Medicine, Roseau, DMA.
Internal Medicine, Ross University School of Medicine, Bowie, USA.
Cureus. 2018 Sep 7;10(9):e3267. doi: 10.7759/cureus.3267.
Apical hypertrophic cardiomyopathy (AHCM) is a rare form of non-obstructive hypertrophic cardiomyopathy. It is rarely reported in African American patients, and more commonly reported in Japanese patients. AHCM involves hypertrophy of the apex of the left ventricle. It is considered to have a benign prognosis in terms of cardiovascular mortality, however arrhythmias and sudden cardiac death have been reported. We report a case of a 49-year-old African American male with a history of hypertension, who presented to the emergency department after in field defibrillation for ventricular fibrillation cardiac arrest with return of spontaneous circulation after 10 minutes of cardiopulmonary resuscitation. Features of left ventricular hypertrophy and deep T-wave inversions in V3-V6 were noted on a 12-lead electrocardiogram which were suggestive of AHCM. Left heart catheterization with left ventriculography and coronary angiography confirmed the diagnosis of AHCM with the classic "ace of spades" sign. This case highlights the rare occurrence of AHCM with ventricular fibrillation cardiac arrest in an African American male, treated with hypertension management, aspirin, atorvastatin and automated implantable cardioverter-defibrillator placement.
心尖肥厚型心肌病(AHCM)是一种罕见的非梗阻性肥厚型心肌病。在非裔美国患者中鲜有报道,而在日本患者中报道更为常见。AHCM累及左心室心尖部肥厚。就心血管死亡率而言,其预后被认为是良性的,然而已有心律失常和心源性猝死的报道。我们报告一例49岁有高血压病史的非裔美国男性病例,该患者在现场因心室颤动心脏骤停接受除颤治疗,经10分钟心肺复苏后恢复自主循环,随后被送往急诊科。12导联心电图显示左心室肥厚及V3 - V6导联T波深倒置,提示AHCM。左心导管检查及左心室造影和冠状动脉造影通过典型的“黑桃A”征确诊为AHCM。该病例突出了非裔美国男性发生AHCM合并心室颤动心脏骤停的罕见情况,并接受了高血压管理、阿司匹林、阿托伐他汀治疗及植入式自动心脏复律除颤器植入。