[Gastrointestinal manifestations of recessive dystrophic epidermolysis bullosa].

The clinical charts of eight children with gastrointestinal symptomatology secondary to recessive dystrophic epidermolysis bullosa are reviewed. The most frequently found gastrointestinal lesions were esophageal stricture (6 patients), a repeated history of ampullar lesions (8 patients), constipation (5) and anchiloglossia (2). The most frequent and feared lesion is the esophageal stricture. Esophageal stricture; epidermolysis; gastrointestinal manifestations.