慢性炎症性脱髓鞘性多发性神经病的不寻常特征：长期通气支持后预后良好。
Unusual features in chronic inflammatory demyelinating polyneuropathy: Good outcome after prolonged ventilatory support.
作者信息
Jha Sanjeev, Ansari Mk, Sonkar Kk, Paliwal Vk
机构信息
Department of Neurology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India.
出版信息
J Neurosci Rural Pract. 2011 Jul;2(2):171-3. doi: 10.4103/0976-3147.83586.
Severe respiratory muscle paralysis and ventilatory failure is rare in chronic inflammatory demyelinating polyneuropathy (CIDP). We report a 14 year child who presented with respiratory failure, bulbar and multiple cranial nerves involvement along with bilateral phrenic nerve paralysis. He was diagnosed with CIDP after electrophysiological evaluation. He required AMBU ventilation for about 4 months (including domiciliary use), after which he recovered significantly. Along with several unusual features of CIDP, this report highlights good example of steady basic intensive care to save lives and rewarding outcome of prolonged respiratory support, provided by AMBU ventilation which is a rather primitive, but inexpensive device.
严重呼吸肌麻痹和呼吸衰竭在慢性炎症性脱髓鞘性多发性神经病（CIDP）中较为罕见。我们报告一名14岁儿童，其表现为呼吸衰竭、延髓及多条颅神经受累以及双侧膈神经麻痹。经电生理评估后，他被诊断为CIDP。他需要使用急救复苏球囊通气约4个月（包括居家使用），之后病情显著好转。除了CIDP的一些不寻常特征外，本报告还突出了一个很好的例子，即通过稳定的基础重症护理来挽救生命，以及使用急救复苏球囊通气（一种相当原始但价格低廉的设备）进行长期呼吸支持所带来的良好结果。
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