Machado Guilherme, Di Rocco Federico, Sainte-Rose Christian, Meyer Philippe, Marchac Daniel, Macquet-Nouvion Gaëlle, Arnaud Eric, Renier Dominique
Department of Pediatric Neurosurgery, Hôpital Necker-Enfants Malades, Paris, France.
Childs Nerv Syst. 2011 Oct;27(10):1683-91. doi: 10.1007/s00381-011-1508-8. Epub 2011 Sep 17.
This article describes the clinical aspects for both operated and non-operated patients with a cloverleaf skull deformity treated in our service, focusing on hydrocephalus.
We describe 13 cases of cloverleaf skull deformity treated in our services between 1977 and 2008. Among them, ten were operated (9 out of 13 for the craniofacial stenosis and 7 out of 13 for hydrocephalus).
Hydrocephalus was present in all patients with bilateral lambdoid stenosis. There was no case of hydrocephalus among the patients with unilateral or absent lambdoid stenosis. Associated malformations and severe faciostenosis were associated with higher mortality and morbidity.
The development of hydrocephalus seems to be closely related to a bilateral lambdoid stenosis. The optimal treatment must be tailored individually considering the degree of the malformation and the presence of complications and comorbidities.
本文描述了在我们科室接受治疗的三叶形颅骨畸形手术和未手术患者的临床情况，重点关注脑积水。
我们描述了1977年至2008年间在我们科室治疗的13例三叶形颅骨畸形病例。其中，10例接受了手术（13例中有9例因颅面狭窄，13例中有7例因脑积水）。
所有双侧人字缝狭窄患者均存在脑积水。单侧或无人字缝狭窄的患者中无一例发生脑积水。相关畸形和严重面部狭窄与较高的死亡率和发病率相关。
脑积水的发生似乎与人字缝双侧狭窄密切相关。必须根据畸形程度以及并发症和合并症的情况进行个体化的最佳治疗。
