Chitnis M, Lazarus C, Simango I, Elsen M, Rensburg C Van, Delft D Von, Tovell Trollope L
Departmet of Paediatrics Surgeryand Dietetics, East London Hospital Complex and Walter Sisulu University, East London, E Cape.
S Afr J Surg. 2011 Mar 14;49(1):44-6.
African degenerative leiomyopathy (ADL) is a rare incurable disorder seen in African children, predominantly in southern and south-eastern Africa. ADL presents as chronic intestinal pseudo-obstruction. Management is traditionally conservative, with surgery restricted to the management of complications. We have placed Malone antegrade continence enema (MACE) stomas in the grossly dilated colon to vent accumulated gas and administer antegrade bowel enemas. This is done mainly for relief of gaseous distension and constipation in an attempt to provide symptomatic relief and improve quality of life. In this article, we present our preliminary results of laparoscopically assisted technique to insert a Mic-Key gastrostomy device as a 'button colostomy' in 8 patients over the past 6½ years.
非洲退行性平滑肌瘤病（ADL）是一种在非洲儿童中罕见的不治之症，主要见于非洲南部和东南部。ADL表现为慢性假性肠梗阻。传统上采用保守治疗，手术仅限于处理并发症。我们已在严重扩张的结肠中放置马龙顺行性节制灌肠（MACE）造口，以排出积聚的气体并进行顺行性肠道灌肠。这样做主要是为了缓解气体膨胀和便秘，试图缓解症状并改善生活质量。在本文中，我们展示了过去6年半里在8例患者中通过腹腔镜辅助技术插入Mic-Key胃造口装置作为“纽扣式结肠造口术”的初步结果。
