Department of Prosthodontics, School of Dentistry, Zahedan, Iran.
J Prosthodont. 2011 Dec;20(8):643-8. doi: 10.1111/j.1532-849X.2011.00768.x. Epub 2011 Oct 4.
Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder. The oral manifestations of the syndrome include rapidly progressive periodontal disease resulting in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age and require prosthodontic treatment. This report is the oral rehabilitation of an edentulous 21-year-old woman with PLS. Treatment included maxillary and mandibular fixed prostheses supported by osseointegrated dental implants. At the 4-year follow-up, the patient presented significant improvements in oral function and psychosocial activities and no prosthetic complications.
牙周病-掌跖角化综合征（PLS）是一种罕见的常染色体隐性遗传疾病。该综合征的口腔表现包括迅速进展的牙周病，导致乳牙和恒牙过早脱落。患者通常在早年就无牙，并需要进行修复治疗。本报告介绍了一例 PLS 牙列缺失女性的口腔修复治疗。治疗包括上颌和下颌固定义齿修复，由骨整合种植牙支持。在 4 年的随访中，患者口腔功能和社会心理活动有显著改善，且无修复体并发症。
