Department of Oral and Maxillofacial Surgery, Erciyes University Faculty of Dentistry, Kayseri, Turkey.
Implant Dent. 2010 Oct;19(5):394-9. doi: 10.1097/ID.0b013e3181ed0798.
Papillon-Lefevre syndrome (PLS) is an autosomal recessive disorder. Main features of PLS are hyperkeratosis of palms and soles concomitant with premature loss of primary and permanent dentition due to progressive periodontitis. Dental management of patients with PLS is usually challenging because of early excessive loss of alveolar bone support. We describe dental rehabilitation of a 34-year-old patient with PLS with severely atrophic mandible by means of 2 short (6 mm) dental implants between 2 mental foramina supporting an implant retained complete denture. After 1 year of follow-up period, the patient was doing well and there was no sign of bone resorption. In patients with PLS, dental osseointegrated implants (even with shorter lengths) can be safely used for atrophic mandibles instead of invasive preprosthetic applications such as bone augmentation, nerve lateralization, or alveolar distraction to avoid possible complications.
掌跖角化过度-牙周病综合征(PLS)是一种常染色体隐性遗传病。PLS 的主要特征是手掌和脚底过度角化,同时由于进行性牙周炎,原发性和永久性牙齿过早缺失。由于牙槽骨支持的早期过度丧失,PLS 患者的牙科管理通常具有挑战性。我们通过在两个颏孔之间放置两个短(6 毫米)的牙科种植体,为一名 34 岁的 PLS 患者下颌严重萎缩进行了牙齿修复,种植体支撑着一副种植体固位的全口义齿。经过 1 年的随访,患者情况良好,没有骨吸收的迹象。对于 PLS 患者,即使使用较短长度的牙科骨整合种植体,也可以安全地用于下颌萎缩,而无需进行侵入性的术前应用,如骨增量、神经侧化或牙槽骨牵张,以避免可能的并发症。