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表现为心源性休克的低钙血症性心肌病。

Hypocalcemic cardiomyopathy presenting as cardiogenic shock.

作者信息

Gupta Pankaj, Tomar Munesh, Radhakrishnan Sitaraman, Shrivastava Savitri

机构信息

Department of Pediatrics and Congenital Heart Surgery, Escorts Heart Institute and Research Centre, New Delhi, India.

出版信息

Ann Pediatr Cardiol. 2011 Jul;4(2):152-5. doi: 10.4103/0974-2069.84655.

Abstract

Hypocalcemia is a less known but treatable cause for dilated cardiomyopathy, leading to severe heart failure in children. Cardiogenic shock related to hypocalcemic cardiomyopathy is a rare event. We describe 5 infants presenting with cardiogenic shock over 3 years, who were found to have severe hypocalcemia as a sole cause of myocardial dysfunction. The patients responded to calcium and vitamin D supplementation promptly and left ventricular systolic function normalized within months of treatment. In any case of cardiogenic shock, hypocalcemia should be included in the differential diagnosis and must be investigated.

摘要

低钙血症是扩张型心肌病鲜为人知但可治疗的病因,可导致儿童严重心力衰竭。与低钙血性心肌病相关的心源性休克是一种罕见事件。我们描述了3年内出现心源性休克的5例婴儿,他们被发现严重低钙血症是心肌功能障碍的唯一原因。这些患者对补充钙和维生素D反应迅速,治疗数月内心室收缩功能恢复正常。在任何心源性休克病例中,鉴别诊断都应考虑低钙血症,且必须进行相关检查。

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Myocardial dysfunction due to hypocalcemia.低钙血症引起的心肌功能障碍。
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