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未经治疗的甲状旁腺功能减退所致的低钙血症性心肌病。

Hypocalcemic cardiomyopathy due to untreated hypoparathyroidism.

作者信息

Altunbaş Hasan, Balci Mustafa K, Yazicioğlu Gökhan, Semiz Ender, Ozbilim Gülay, Karayalçin Umit

机构信息

Department of Internal Medicine, Division of Endocrinology and Metabolism, Akdeniz University School of Medicine, Antalya, Turkey.

出版信息

Horm Res. 2003;59(4):201-4. doi: 10.1159/000069324.

DOI:10.1159/000069324
PMID:12649575
Abstract

Hypocalcemic cardiomyopathy due to hypoparathyroidism is a very rare condition which is usually refractory to conventional treatment for cardiac failure but which responds favorably to restoration of normocalcemia. A 55-year-old man and a 46-year-old woman with a history of postoperative hypoparathyroidism presented with symptoms of cardiac failure and hypocalcemia. A presumptive diagnosis of dilated cardiomyopathy was considered by echocardiography and endomyocardial biopsies were consistent with cardiomyopathy. The coronary angiograms were normal and there was no apparent cause for dilated cardiomyopathy in these patients. The history of the patients and partial recovery of cardiac function after restoration of normocalcemia suggest that hypocalcemia was the cause of dilated cardiomyopathy.

摘要

甲状旁腺功能减退所致的低钙血症性心肌病是一种非常罕见的疾病,通常对心力衰竭的传统治疗无效,但对恢复正常血钙水平反应良好。一名55岁男性和一名46岁女性有术后甲状旁腺功能减退病史,出现心力衰竭和低钙血症症状。超声心动图考虑为扩张型心肌病的初步诊断,心内膜心肌活检结果与心肌病相符。冠状动脉造影正常,这些患者没有明显的扩张型心肌病病因。患者的病史以及恢复正常血钙水平后心功能部分恢复表明,低钙血症是扩张型心肌病的病因。

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ESC Heart Fail. 2025 Feb;12(1):708-716. doi: 10.1002/ehf2.15041. Epub 2024 Sep 10.
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