Singh Paramdeep, Ahluwalia Archana, Saggar Kavita, Grewal Charanpreet Singh
Department of Radiodiagnosis, Dayanand Medical College and Hospital, Ludhiana, Punjab, India.
J Pediatr Neurosci. 2011 Jan;6(1):27-8. doi: 10.4103/1817-1745.84402.
A 15-year-old boy presented with coarse tremors of right hand and dysarthric speech. Neurologic examination demonstrated Kayser-Fleischer rings and dystonic tremor of the right hand. Serum ceruloplasmin and urine copper studies established the diagnosis of Wilson's disease. Brain MRI showed bilateral T2 hyperintensity involving putamen, thalami, and brainstem. Involvement of brainstem revealed the characteristic "double panda sign."
一名15岁男孩出现右手粗大震颤和构音障碍。神经系统检查发现有Kayser-Fleischer环及右手张力障碍性震颤。血清铜蓝蛋白和尿铜检查确诊为威尔逊病。脑部磁共振成像显示双侧壳核、丘脑和脑干T2高信号。脑干受累表现出特征性的“双熊猫征”。
