Masruha Marcelo R, Fialho Libânia M N, da Nóbrega Marcel V, Lin Jaime, Pinho Ricardo S, Cavalheiro Sérgio, Vilanova Luiz Celso P
Department of Neurology and Neurosurgery, Federal University of São Paulo, São Paulo, Brazil.
J Pediatr Neurosci. 2011 Jan;6(1):72-3. doi: 10.4103/1817-1745.84415.
Hemifacial spasm is a disorder of the seventh cranial nerve, which is characterized by irregular, involuntary and recurrent tonic and clonic contractions of the ipsilateral facial expression muscles. This disorder affects mainly adults, and there are few cases reported in childhood. The main etiologies are vascular problems, although tumors are an important cause of hemifacial spasm via a direct or an indirect mass effect. We report a 6-year-old girl who presented with right hemifacial spasm. Magnetic resonance imaging showed a lesion in the cerebellopontine angle, extending from the midbrain to the pons with a slight mass effect on the fourth ventricle. The histological examination revealed a pilocytic astrocytoma.
面肌痉挛是一种第七颅神经疾病,其特征为同侧面部表情肌出现不规则、不自主且反复发作的强直性和阵挛性收缩。这种疾病主要影响成年人,儿童病例报道较少。主要病因是血管问题,尽管肿瘤通过直接或间接的占位效应也是面肌痉挛的重要病因。我们报告一名6岁女童,她出现右侧面肌痉挛。磁共振成像显示桥小脑角有一病变,从中脑延伸至脑桥,对第四脑室有轻微占位效应。组织学检查显示为毛细胞型星形细胞瘤。