Rheumatology Unit, Department of Internal Medicine, University of Modena e Reggio Emilia, Medical School, Via del Pozzo, 71, 41121 Modena, Italy.
Clin Rheumatol. 2012 Jan;31(1):183-7. doi: 10.1007/s10067-011-1866-3. Epub 2011 Oct 12.
Eosinophilic fasciitis (EF) is a rare disease characterized by symmetrical thickness and hardening of the skin, especially localized to forearms and thorax, with eosinophilia. Corticosteroids represent the first-line therapy, even if some patients are scarcely responsive and/or may develop important side effects due to long-term treatment. Here, we describe three cases of EF, two of them refractory to previous steroid therapy, successfully treated with D-penicillamine. The present clinical observations together with the updated review of the literature suggest usefulness of D-penicillamine in EF patients, as well as its potential steroid-sparing value.
嗜酸性筋膜炎(EF)是一种罕见疾病,其特征为皮肤对称性增厚和硬化,尤其是前臂和胸部,伴有嗜酸性粒细胞增多。皮质类固醇是一线治疗方法,即使有些患者反应不佳,和/或由于长期治疗可能会出现重要的副作用。在这里,我们描述了三例 EF 病例,其中两例对先前的类固醇治疗有抗药性,用 D-青霉胺成功治疗。目前的临床观察结果以及对文献的最新回顾表明,D-青霉胺在 EF 患者中的有效性,以及其潜在的类固醇节约价值。