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[镰状细胞病伴溶血性危机的危及生命的急性胸部综合征。采用静脉-静脉体外膜肺氧合(ECMO)治疗]

[Life-threatening acute chest syndrome with hemolytic crisis in sickle cell disease. Treatment using a venovenous extracorporeal membrane oxygenation (ECMO)].

作者信息

Hoffmann M, Geldner G, Leschke M

机构信息

Klinik für Anästhesie, Intensivmedizin, Schmerztherapie und Notfallmedizin, Klinikum Ludwigsburg.

出版信息

Dtsch Med Wochenschr. 2011 Oct;136(43):2192-5. doi: 10.1055/s-0031-1292031. Epub 2011 Oct 18.

DOI:10.1055/s-0031-1292031
PMID:22009171
Abstract

HISTORY AND CLINICAL FINDINGS

A 28-year-old male patient with sickle cell disease developed a vasoocclusive crisis with an acute chest syndrome and severe lung failure.

TREATMENT AND COURSE

After partial substitution transfusion the patient was successfully treated extracorporeal membrane oxygenation (ECMO). After 12 days he was weaned from the ECMO, 2 days later the patient's tracheostoma was removed. 19 days after the event the patient had recovered completely and was moved to a hospital in Paris from where he came.

CONCLUSION

Apparently data is sparse regarding the use of ECMO for treatment of a life-threatening acute chest syndrome in sickle cell disease. However, the therapy approach seems to be promising and is worth considering in this particular situation.

摘要

病史及临床发现

一名28岁患有镰状细胞病的男性患者发生血管闭塞性危机,伴有急性胸部综合征和严重肺衰竭。

治疗过程

在进行部分置换输血后,患者成功接受了体外膜肺氧合(ECMO)治疗。12天后,他脱离了ECMO,2天后患者的气管造口被移除。事件发生19天后,患者已完全康复,并被转回他来自的巴黎的一家医院。

结论

显然,关于使用ECMO治疗镰状细胞病危及生命的急性胸部综合征的数据很少。然而,这种治疗方法似乎很有前景,在这种特殊情况下值得考虑。

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引用本文的文献

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Life-Threatening Infectious Complications in Sickle Cell Disease: A Concise Narrative Review.镰状细胞病的危及生命的感染性并发症:简明叙述性综述
Front Pediatr. 2020 Feb 20;8:38. doi: 10.3389/fped.2020.00038. eCollection 2020.
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Spontaneous breathing during extracorporeal membrane oxygenation treatment of sickle cell disease acute chest syndrome.镰状细胞病急性胸综合征体外膜肺氧合治疗期间的自主呼吸。
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