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静脉-静脉体外膜肺氧合在一名镰状细胞贫血合并严重急性胸部综合征成年患者中的成功应用

Successful Use of Veno-Venous Extracorporeal Membrane Oxygenation in an Adult Patient with Sickle Cell Anemia and Severe Acute Chest Syndrome.

作者信息

Sewaralthahab Sarah S, Menaker Jay, Law Jennie Y

机构信息

a Department of Internal Medicine , University of Maryland Medical Center , Baltimore , MD , USA.

b R. Adams Cowley Shock Trauma Center, University of Maryland School of Medicine , Baltimore , MD , USA.

出版信息

Hemoglobin. 2018 Jan;42(1):65-67. doi: 10.1080/03630269.2018.1450755.

DOI:10.1080/03630269.2018.1450755
PMID:29633667
Abstract

A 25-year-old female with sickle cell anemia presented with respiratory failure due to acute chest syndrome (ACS). Given her severely compromised cardiopulmonary status, she was started on veno-venous extracorporeal membrane oxygenation (VV-ECMO). After 20 days, the patient's respiratory status improved and she was successfully decannulated. Veno-venous extracorporeal membrane oxygenation can be utilized for severe ACS in adult patients with sickle cell disease. Prompt initiation of this modality may improve outcomes in adult patients with sickle cell disease complicated by life threatening ACS.

摘要

一名25岁患有镰状细胞贫血的女性因急性胸综合征(ACS)出现呼吸衰竭。鉴于其严重受损的心肺状况,她开始接受静脉-静脉体外膜肺氧合(VV-ECMO)治疗。20天后,患者的呼吸状况改善,成功拔除插管。静脉-静脉体外膜肺氧合可用于患有镰状细胞病的成年患者的严重ACS。及时启动这种治疗方式可能会改善患有危及生命的ACS并发症的镰状细胞病成年患者的预后。

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引用本文的文献

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Spontaneous breathing during extracorporeal membrane oxygenation treatment of sickle cell disease acute chest syndrome.镰状细胞病急性胸综合征体外膜肺氧合治疗期间的自主呼吸。
Respir Med Case Rep. 2019 Aug 14;28:100924. doi: 10.1016/j.rmcr.2019.100924. eCollection 2019.