Nakamura Hiroki, Okazaki Tadaharu, Koga Hiroyuki, Lane Geoffrey J, Yamataka Atsuyuki
Department of Pediatric General and Urogenital Surgery, Juntendo University School of Medicine, Tokyo, 113-8421, Japan.
Pediatr Surg Int. 2012 Jan;28(1):63-6. doi: 10.1007/s00383-011-3000-7.
We report a male infant with severe brachioesophagus with intrathoracic stomach, duodenum, pancreas, and spleen associated with short neck because of rachischisis and scoliosis, an extremely rare condition described recently as "serpentine-like syndrome". Our case died and we review four similar cases reported in the English literature.