Mochizuki Kyoko, Obatake Masayuki, Takatsuki Mitsuhisa, Nakatomi Akiko, Hayashi Tomayoshi, Okudaira Sadayuki, Eguchi Susumu
Division of Pediatric Surgery, Department of Surgery, Nagasaki University Graduate School of Biomedical Sciences, 1-7-1 Sakamoto, Nagasaki, 852-8501, Japan.
Pediatr Surg Int. 2012 Jan;28(1):51-4. doi: 10.1007/s00383-011-3018-x.
We herein report a case of progressive familial intrahepatic cholestasis with partial internal biliary diversion (PIBD). Although by using PIBD an external stoma can be avoided, exposure of the ileocecal junction to bile reflux as well as the effects of the direct bile flow on the colonic mucosa require further investigation.
我们在此报告一例伴有部分肝内胆管转流术(PIBD)的进行性家族性肝内胆汁淤积症。尽管通过使用PIBD可以避免外部造口,但回盲部暴露于胆汁反流以及胆汁直接流动对结肠黏膜的影响仍需进一步研究。