Nawaz S, Dobersen M J, Blount S G, Firminger H I, Petty T L
Department of Pathology, University of Colorado Health Sciences Center, Denver.
Chest. 1990 Oct;98(4):1037-9. doi: 10.1378/chest.98.4.1037.
A young woman presented with rapidly progressive dyspnea and clinical findings strongly suggestive of primary pulmonary hypertension or possible pulmonary embolism (or both). She died of acute right-sided heart failure. A diagnosis of pulmonary veno-occlusive disease was made at autopsy. Approximately 100 cases of this disease have been reported previously in the literature. We describe a patient with a particularly florid progression of this unusual disease. Death occurred within six weeks of the onset of symptoms.
一名年轻女性出现快速进展的呼吸困难，临床检查结果强烈提示原发性肺动脉高压或可能的肺栓塞（或两者兼有）。她死于急性右侧心力衰竭。尸检诊断为肺静脉闭塞性疾病。此前文献中已报道了约100例该疾病。我们描述了一名患有这种罕见疾病且病情进展特别严重的患者。症状出现后六周内死亡。
