一名患有肺静脉闭塞病（PVOD）和重度肺动脉高压患者的猝死
Sudden Death in a Patient with Pulmonary Veno-occlusive Disease (PVOD) and Severe Pulmonary Hypertension.
作者信息
Saito Minako, Ohshima Nobuharu, Matsui Hirotoshi, Hebisawa Akira, Ohta Ken
机构信息
Center for Pulmonary Diseases, National Hospital Organization Tokyo National Hospital, Japan.
Asthma and Allergy Center, National Hospital Organization Tokyo National Hospital, Japan.
出版信息
Intern Med. 2017;56(15):2025-2031. doi: 10.2169/internalmedicine.56.7869. Epub 2017 Aug 1.
A 58-year-old woman was referred to our hospital with a chief complaint of exertional dyspnea. Bronchoscopy failed to establish a diagnosis, and the patient subsequently died suddenly due to respiratory insufficiency because of advanced pulmonary hypertension (PH). The pathological diagnosis at autopsy was pulmonary veno-occlusive disease (PVOD). PVOD is difficult to diagnose antemortem and has a poor prognosis. Lung transplantation is the only curative treatment for PVOD.
一名58岁女性因劳力性呼吸困难为主诉被转诊至我院。支气管镜检查未能明确诊断，随后该患者因晚期肺动脉高压（PH）导致呼吸功能不全而突然死亡。尸检病理诊断为肺静脉闭塞性疾病（PVOD）。PVOD生前难以诊断且预后较差。肺移植是PVOD唯一的治愈性治疗方法。
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