Imamura Takashi, Momoi Nobuo, Go Hayato, Ogasawara Kei, Sato Maki, Hosoya Mitsuaki
Department of Pediatrics, Fukushima Medical University School of Medicine, Japan.
Congenit Anom (Kyoto). 2011 Dec;51(4):187-90. doi: 10.1111/j.1741-4520.2011.00321.x.
Isolated levocardia (IL) is a rare type of situs inversus in which the heart is in the normal left-side position, but the abdominal viscera are in the dextroposition. Polysplenia is a congenital disorder affecting the asymmetric organs, including the heart, lungs, bronchi, liver, stomach, intestines, and spleen. In this report, we present a rare type satisfying the characteristics of both IL and polysplenia, confirmed by several imaging investigations, which revealed normally structured lungs and heart and the existence of the inferior vena cava (IVC), which runs on the left side, returns to the anterior-right side at the liver, and returns to the right atrium directly. Anatomical investigation and careful observation will make it possible to improve the prognosis of IL.
孤立性左位心（IL）是一种罕见的内脏反位类型，其中心脏位于正常的左侧位置，但腹部脏器处于右旋位。多脾综合征是一种影响不对称器官的先天性疾病，这些器官包括心脏、肺、支气管、肝脏、胃、肠道和脾脏。在本报告中，我们呈现了一种罕见类型，它兼具IL和多脾综合征的特征，经多项影像学检查得以证实，这些检查显示肺和心脏结构正常，且存在下腔静脉（IVC），该静脉走行于左侧，在肝脏处回到右前侧，并直接汇入右心房。解剖学研究和仔细观察将有助于改善IL的预后。
