Unit of Thoracic Surgery, Ospedale Civile Maggiore, Verona, Italy.
Ann Thorac Surg. 2011 Dec;92(6):e119-20. doi: 10.1016/j.athoracsur.2011.06.019.
Lipoblastoma is a rare benign tumor arising from embryonic fat; it occurs mainly in the extremities and almost exclusively in infants and children younger than 3 years. We present a case of giant mediastinal lipoblastoma in a 16-month-old boy who presented with acute respiratory distress. The mass was completely excised through a left posterolateral thoracotomy. The postoperative course was uneventful, and the pathologic final diagnosis was lipoblastoma. Although extremely rare, mediastinal lipoblastoma can be life threatening; therefore, it should be included in the differential diagnosis of mediastinal mass in younger subjects.
脂肪母细胞瘤是一种罕见的良性肿瘤，起源于胚胎脂肪；它主要发生在四肢，几乎只发生在 3 岁以下的婴儿和儿童中。我们报告了一例 16 个月大男孩的巨大纵隔脂肪母细胞瘤病例，该男孩表现为急性呼吸窘迫。肿瘤通过左后外侧开胸术完全切除。术后过程顺利，病理最终诊断为脂肪母细胞瘤。尽管极为罕见，但纵隔脂肪母细胞瘤可能危及生命；因此，它应包括在年轻患者纵隔肿块的鉴别诊断中。
