Dogan Riza, Kara Murat, Firat Pinar, Gedikoglu Gokhan
Department of Thoracic Surgery, Hacettepe University Faculty of Medicine, 06100 Ankara, Turkey.
Eur J Cardiothorac Surg. 2007 Feb;31(2):325-7. doi: 10.1016/j.ejcts.2006.11.012. Epub 2006 Dec 11.
Lipoblastomatous tumors are quite rare neoplasms deriving from embryonic white fatty tissues, most often seen in infancy and childhood. Lipoblastoma is the focal and well-circumscribed type, whereas lipoblastomatosis is the more infiltrating type of lipoblastomatous tumors. We present a 14-month-old male infant presenting with a mediastinal mass showing paraparesis, who had previously undergone the removal of the cervical part of this mediastinal mass. We removed the mediastinal part of the mass with a posterolateral thoracotomy which proved to be a lipoblastomatosis. We emphasize that this very uncommon tumor located at the neck and mediastinum should be included in the differential diagnosis of infants having gait disturbance.
脂肪母细胞瘤性肿瘤是一种非常罕见的肿瘤,起源于胚胎白色脂肪组织,多见于婴儿期和儿童期。脂肪母细胞瘤是局灶性且边界清晰的类型,而脂肪母细胞瘤病是脂肪母细胞瘤性肿瘤中浸润性更强的类型。我们报告一例14个月大的男婴,其纵隔肿块导致双下肢轻瘫,此前已切除该纵隔肿块的颈部部分。我们通过后外侧开胸手术切除了肿块的纵隔部分,结果证实为脂肪母细胞瘤病。我们强调,对于有步态障碍的婴儿,鉴别诊断时应考虑这种位于颈部和纵隔的非常罕见的肿瘤。