Neuroscience Institute, Medical Academy, Lithuanian University of Health Sciences, Eivenių 4, 50161 Kaunas, Lithuania.
Medicina (Kaunas). 2011;47(8):440-5. Epub 2011 Nov 18.
Primitive neuroectodermal tumors are a group of rare, aggressive, and highly malignant embryonal tumors of unknown etiology of the central and peripheral nervous systems. It is a term for a group of small round cell tumors thought to be derived from fetal neuroectodermal precursor cells. Primitive neuroectodermal tumor is usually described as a tumor of children younger than 15 years and is very rare in adults. The article presents a short literature review and a rare case of a primary primitive neuroectodermal tumor of the central nervous system diagnosed in a 51-year-old woman.
原始神经外胚层肿瘤是一组罕见的、侵袭性强、高度恶性的中枢和外周神经系统胚胎源性肿瘤,其病因不明。它是一组被认为来源于胎儿神经外胚层前体细胞的小圆细胞肿瘤的统称。原始神经外胚层肿瘤通常被描述为发生于 15 岁以下儿童的肿瘤,在成年人中非常罕见。本文介绍了一篇简短的文献综述和一个罕见的 51 岁女性中枢神经系统原始神经外胚层肿瘤的病例。