Ohta A, Yamaguchi M, Tsunematsu T, Kasukawa R, Mizushima H, Kashiwagi H, Kashiwazaki S, Tanimoto K, Matsumoto Y, Akizuki M
Adult Still's Disease Research Committee, Japan.
J Rheumatol. 1990 Aug;17(8):1058-63.
A comprehensive survey of Japanese patients with adult Still's disease was made by questionnaire which was sent to major institutions with rheumatology units in Japan. Of 146 cases from 32 institutions, 90 were judged to be definitely diagnosed as adult Still's disease. The major clinical features in these 90 patients consisted of high fever, polyarthralgia, rash, increased erythrocyte sedimentation rate, negative autoantibodies, leukocytosis, liver dysfunction, and hyperferritinemia. The incidence of several features showed significant differences between these cases and previous nonJapanese cases.
通过向日本设有风湿病科的主要机构发送调查问卷，对日本成人斯蒂尔病患者进行了全面调查。在来自32个机构的146例病例中，90例被判定为确诊为成人斯蒂尔病。这90例患者的主要临床特征包括高热、多关节痛、皮疹、红细胞沉降率升高、自身抗体阴性、白细胞增多、肝功能障碍和高铁蛋白血症。这些病例与之前的非日本病例相比，几种特征的发生率存在显著差异。
