Galesić Kresimir, Horvatić Ivica, Tisljar Miroslav, Bulimbasić Stela, Bozić Borka, Ljubanović Danica Galesić
Interna klinika, Medicinski fakultet, Sveuciliste u Zagrebu, KB "Dubrava", Zagreb.
Lijec Vjesn. 2011 Sep-Oct;133(9-10):315-9.
Fibrillary glomerulonephritis and immunotactoid glomerulopathy belong to the rare renal disorders characterized by formation of the organized glomerular deposits. Pathogenesis of these disorders is still not fully clarified but they could appear as a primary condition or be regarded as a part of the various systemic mainly lymphoproliferative disorders. Clinical presentation includes proteinuria, hematuria, arterial hypertension and progressive renal insufficiency during several years. In this work we presented a male patient with fibrillary glomerulonephritis and a female patient with immunotactoid glomerulopathy as a part of a non-Hodgkin lymphoma. The aim of this presentation is to show the features of the fibrillary glomerulonephritis and immunotactoid glomerulopathy as well as emphasize the significance of the electron microscopy in the identification of these uncommon entities.
纤维性肾小球肾炎和免疫触须样肾小球病属于罕见的肾脏疾病,其特征为形成有组织的肾小球沉积物。这些疾病的发病机制仍未完全阐明,但它们可以表现为原发性疾病,或被视为各种主要是淋巴增殖性系统疾病的一部分。临床表现包括蛋白尿、血尿、动脉高血压以及数年内逐渐发展的肾功能不全。在这项研究中,我们报告了一名患有纤维性肾小球肾炎的男性患者和一名患有免疫触须样肾小球病且并发非霍奇金淋巴瘤的女性患者。本报告的目的是展示纤维性肾小球肾炎和免疫触须样肾小球病的特征,并强调电子显微镜检查在识别这些罕见疾病中的重要性。