Department of Pediatric Neurology, Karadeniz Technical University Faculty of Medicine, Trabzon.
Epileptic Disord. 2011 Dec;13(4):394-400. doi: 10.1684/epd.2011.0478.
This prospective study was designed to investigate whether or not monotherapy with sodium valproate (VPA) or oxcarbazepine (OXC) affects plasma levels of fatty acylcarnitine esters in children with epilepsy. A total of 56 children with idiopathic partial or generalised epilepsy were included in the study. Patients were assigned to receive either VPA or OXC monotherapy. Free carnitine (C0) and acylcarnitine profiles of the patients were investigated using tandem mass spectrometry at baseline and at six and 18 months after commencement of therapy. For patients receiving VPA or OXC monotherapy, there were no significant differences in plasma levels of C0, compared with baseline, at six and 18 months (p>0.05). Treatment with VPA for six and 18 months correlated with a significant increase in 3-hydroxy-isovalerylcarnitine (C5-OH) (six months: +23%; 18 months: +73%), and significant decreases in the following acylcarnitines: C6-acylcarnitine (six months: -60%; 18 months: -66%), C14-acylcarnitine (six months: -25%; 18 months: -38%), C16-acylcarnitine (six months: -73%; 18 months: -73%), and C18:1-OH-acylcarnitine (six months: -60%; 18 months: -70%), compared with baseline (p<0.05). In patients receiving OXC monotherapy, on the other hand, plasma concentrations (μmol/L) of acylcarnitines (from C2 to C18:1-OH) fell within the normal reference range. The results of this study indicate that there are significant biochemical changes in acylcarnitines in ambulatory children on VPA monotherapy but these are not clinically significant. OXC monotherapy had no effect on acylcarnitine metabolism in ambulatory children.
本前瞻性研究旨在探讨单药治疗丙戊酸钠(VPA)或奥卡西平(OXC)是否会影响癫痫儿童的血浆脂肪酸酰基肉碱酯水平。共有 56 名特发性部分或全身性癫痫患儿纳入本研究。患者被分配接受 VPA 或 OXC 单药治疗。在基线时以及治疗开始后 6 个月和 18 个月,使用串联质谱法研究患者的游离肉碱(C0)和酰基肉碱谱。对于接受 VPA 或 OXC 单药治疗的患者,与基线相比,在 6 个月和 18 个月时,血浆 C0 水平没有显著差异(p>0.05)。VPA 治疗 6 个月和 18 个月与 3-羟基异戊酰肉碱(C5-OH)显著增加相关(6 个月:+23%;18 个月:+73%),并与以下酰基肉碱显著降低相关:C6-酰基肉碱(6 个月:-60%;18 个月:-66%)、C14-酰基肉碱(6 个月:-25%;18 个月:-38%)、C16-酰基肉碱(6 个月:-73%;18 个月:-73%)和 C18:1-OH-酰基肉碱(6 个月:-60%;18 个月:-70%),与基线相比(p<0.05)。另一方面,接受 OXC 单药治疗的患者,酰基肉碱(从 C2 到 C18:1-OH)的血浆浓度(μmol/L)在正常参考范围内。这项研究的结果表明,在接受 VPA 单药治疗的门诊儿童中,酰基肉碱存在显著的生化变化,但这些变化没有临床意义。OXC 单药治疗对门诊儿童的酰基肉碱代谢没有影响。