夫妻性肌萎缩侧索硬化症
Conjugal amyotrophic lateral sclerosis.
作者信息
Dewitt John D, Kwon Julia, Burton Rebecca, Stroup Jeffrey S
机构信息
Department of Internal Medicine, Oklahoma State University Medical Center, Tulsa, Oklahoma (Kwon, Burton, Stroup). Dr. Dewitt is a neurologist in private practice in Tulsa, Oklahoma.
出版信息
Proc (Bayl Univ Med Cent). 2012 Jan;25(1):31-3. doi: 10.1080/08998280.2012.11928778.
Abstract
Amyotrophic lateral sclerosis (ALS) is a disease characterized by progressive degeneration of motor neurons in the motor cortex, brainstem, and spinal cord. The incidence of sporadic ALS is 1.5 to 2.7 in 100,000, and the prevalence is 5.2 to 6.0 in 100,000. Conjugal ALS is even rarer than sporadic ALS. We report a case of conjugal ALS encountered in our outpatient neurology clinic.
摘要
肌萎缩侧索硬化症（ALS）是一种以运动皮层、脑干和脊髓中的运动神经元进行性退变为特征的疾病。散发性ALS的发病率为十万分之1.5至2.7，患病率为十万分之5.2至6.0。夫妻双方均患ALS的情况比散发性ALS更为罕见。我们报告了在我们神经内科门诊遇到的一例夫妻双方均患ALS的病例。
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