Ammouche C, Moog R, Lacreuse I, Gomes C, Kauffmann I, Becmeur F
Service de pédiatrie, CHU Hautepierre, 67098 Strasbourg, France.
Arch Pediatr. 2012 Mar;19(3):260-3. doi: 10.1016/j.arcped.2011.12.019. Epub 2012 Feb 3.
We report the case of an infant who underwent surgery on the first day of life for a giant omphalocele. At the age of 16 months, he presented an acute abdominal syndrome and died a few hours later. Autopsy revealed a twisted left liver lobe (LL) including a suprahepatic vein. To our knowledge, this is the first case of giant omphalocele complicated by twisted liver lobe and fatal outcome.