Fijałkowska Marta, Antoszewski Bogusław
Department of Plastic, Reconstructive and Aesthetic Surgery Second Chair of Surgery, Medical University, Łódź.
Pol Przegl Chir. 2011 Dec;83(12):662-7. doi: 10.2478/v10035-011-0106-5.
Poland's syndrome is characterized by variable clinical picture. Classic deformity consists of unilateral hypoplasia or aplasia of the sternocostal head of the pectoralis major muscle and ipsilateral hand malformations. Additionally on the affected side hypoplasia or aplasia of the breast in women is observed. Variable malformations in Poland's syndrome cause that there is no uniform treatment schedule. THE AIM OF THE STUDY was to analyze surgical treatment conducted in patients with Poland's syndrome in Plastic, Reconstructive and Aesthetic Surgery Clinic.
A retrospective analysis of surgical treatment was carried out in the group of 66 patients with Poland's syndrome on the basis of their medical documentation.
The most common operation performed in women was breast reconstruction with silicone implant. Two men had their chest symmetrized by fat grafting. Syndactyly observed in patients with complete Poland's syndrome was surgically removed in early childhood.
Treatment of patients with Poland's syndrome, mainly due to variable clinical picture, is individual and depends on age, sex and degree of deformity. In children with complete Poland's syndrome operations include surgical removing of syndactyly. Breast reconstruction in women with Poland's syndrome with silicone implants is known and safe method. Such procedures are performed after 18 years of age.
波兰综合征的临床表现多样。典型畸形包括胸大肌胸肋头的单侧发育不全或缺失以及同侧手部畸形。此外,在患侧可观察到女性乳房发育不全或缺失。波兰综合征的多种畸形导致不存在统一的治疗方案。本研究的目的是分析在整形、重建与美容外科诊所对波兰综合征患者进行的手术治疗。
基于66例波兰综合征患者的医疗记录,对其手术治疗进行回顾性分析。
女性最常进行的手术是硅胶植入乳房重建。两名男性通过脂肪移植使胸部对称。完全性波兰综合征患者出现的并指畸形在儿童早期通过手术切除。
波兰综合征患者的治疗主要因其临床表现多样而个体化,取决于年龄、性别和畸形程度。对于完全性波兰综合征儿童,手术包括并指切除术。硅胶植入对波兰综合征女性进行乳房重建是一种已知且安全的方法。此类手术在18岁以后进行。