Bushe K A, Naumann M, Warmuth-Metz M, Meixensberger J, Müller J
Department of Neurosurgery, University of Würzburg, Federal Republic of Germany.
Neurosurgery. 1990 Oct;27(4):625-8. doi: 10.1097/00006123-199010000-00020.
Maffucci's syndrome is characterized by the combination of multiple enchondromas (Ollier's disease) and hemangiomatosis. These hemangiomas develop in the subcutaneous tissue and form red-blue tumors dispersed over the whole body. Intracranial involvement is rare, making a preoperative radiological diagnosis and differentiation from other tumors rather difficult. The radiological characteristics and successful removal of the intracranial part of a chondrosarcoma of the cerebellopontine angle in a case of Maffucci's syndrome are reported in this paper.
