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外阴硬化性苔藓、溃疡性皮肤钙化症和皮肌炎并存:巧合还是免疫机制?

The co-existence of vulvar lichen sclerosus, ulcerated calcinosis cutis, and dermatomyositis: coincidence or immunological mechanism?

作者信息

Balcı Didem Didar, Celik Ebru, Sarıkaya Gökhan, Yenin Jülide Zehra, Atik Esin

机构信息

Department of Dermatology, Faculty of Medicine, Mustafa Kemal University, Antakya-Hatay, Turkey.

出版信息

Ann Dermatol. 2011 Dec;23(Suppl 3):S375-9. doi: 10.5021/ad.2011.23.S3.S375. Epub 2011 Dec 27.

DOI:10.5021/ad.2011.23.S3.S375
PMID:22346282
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3276801/
Abstract

Calcinosis cutis is a condition characterized by the deposition of calcium salts in the skin and subcutaneous tissues, and patients suffering from it encounter various connective tissue disorders, such as dermatomyositis (DM), scleroderma, and systemic lupus erythematosus. Although calcinosis cutis is frequently accompanied by juvenile dermatomyositis, rare cases have been reported in adult patients with DM. On the other hand, lichen sclerosus (LS) is a chronic inflammatory disease of the skin and mucosal surfaces. In the present report, we present a rare case of a 71-year-old patient with DM accompanied by ulcerated calcinosis cutis and vulvar LS.

摘要

皮肤钙化症是一种以钙盐沉积于皮肤和皮下组织为特征的病症,患有该病的患者会遭遇各种结缔组织疾病,如皮肌炎(DM)、硬皮病和系统性红斑狼疮。虽然皮肤钙化症常伴有幼年皮肌炎,但成年DM患者中也有罕见病例的报道。另一方面,硬化性苔藓(LS)是一种皮肤和黏膜表面的慢性炎症性疾病。在本报告中,我们呈现了一例罕见病例,一名71岁的患者患有DM,同时伴有溃疡性皮肤钙化症和外阴LS。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/b9ce7787dc5f/ad-23-S375-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/a5c0817a30b7/ad-23-S375-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/6500cd55721d/ad-23-S375-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/34c61fa0173e/ad-23-S375-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/9b15e9916274/ad-23-S375-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/06639e30ef7a/ad-23-S375-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/b9ce7787dc5f/ad-23-S375-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/a5c0817a30b7/ad-23-S375-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/6500cd55721d/ad-23-S375-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/34c61fa0173e/ad-23-S375-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/9b15e9916274/ad-23-S375-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/06639e30ef7a/ad-23-S375-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d2d7/3276801/b9ce7787dc5f/ad-23-S375-g006.jpg

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