Department of Anesthesiology and Reanimation, Medical Faculty, Selcuk University, Akyokus, Meram, Konya, Turkey.
J Anesth. 2012 Apr;26(2):283-5. doi: 10.1007/s00540-011-1309-y. Epub 2012 Feb 22.
Arthrogryposis multiplex congenita (AMC) consists of complex congenital anomalies characterized by multiple contractures. Anesthetic management of these patients requires special care: as this disease often progresses until dysfunction of multiple organ systems occur, it may have an impact on the anesthetic management. Here, we report a case of AMC undergoing urgent surgery for open tibia fracture who had difficult airway management because of limited mouth opening. The anesthetic management of this patient is represented in light of the literature.
先天性多发性关节挛缩症（AMC）由多种先天性畸形引起，表现为多个关节挛缩。此类患者的麻醉管理需要特别注意：由于该病常进展至多器官系统功能障碍，故可能会对麻醉管理产生影响。本研究报告了 1 例因开放性胫骨骨折行急症手术且因张口度受限致气道管理困难的 AMC 患者。本研究结合文献报道了该患者的麻醉管理过程。
