Oberoi G S, Kaul H L, Gill I S, Batra R K
Can J Anaesth. 1987 May;34(3 ( Pt 1)):288-90. doi: 10.1007/BF03015167.
The anaesthetic management of an 11-year-old male with arthrogryposis multiplex congenita (AMC) with myopathic features is described. The child presented with an obstructing renal calculus and a pyelolithotomy via an anterior transverse subcostal extraperitoneal incision was performed. In view of the associated hypoplastic musculature, severe scoliosis and expected increased sensitivity to various sedatives and inhalational anaesthetic agents, low-dose ketamine (10-15 micrograms X kg-1 X min-1) was administered by continuous infusion, with a satisfactory result.
本文描述了一名患有先天性多发性关节挛缩症（AMC）且具有肌病特征的11岁男性患者的麻醉管理情况。该患儿因肾结石梗阻入院，通过前外侧肋下经腹膜外切口进行了肾盂切开取石术。鉴于其伴有肌肉发育不全、严重脊柱侧弯以及预计对各种镇静剂和吸入麻醉剂的敏感性增加，通过持续输注给予低剂量氯胺酮（10 - 15微克/千克/分钟），效果良好。
