Dodge-Khatami A, Tsang V, Roebuck D, Elliott M
Senior Surgical Registrar, Cardiothoracic Unit, Great Ormond Street, London.
Images Paediatr Cardiol. 2000 Jan;2(1):29-39.
Congenital tracheal stenosis is a rare but underdiagnosed anomaly which can present as life-threatening respiratory insufficiency in neonates and infants. Initial control of the airway is mandatory. Surgical correction is the mainstay of therapy and is achieved with low mortality. The type and extent of repair depends largely on the length of stenosis. Cardiac anomalies are frequently associated and may be addressed at the time of tracheal surgery. Despite initial satisfactory results, post-operative morbidity due to persistent granulation tissue is substantial. It is through a multidisciplinary approach and close follow-up of the repaired airway that these demanding patients are best cared for. The long-term quality of life remains uncertain.
先天性气管狭窄是一种罕见但易被漏诊的异常情况，可表现为新生儿和婴儿危及生命的呼吸功能不全。气道的初始控制是必不可少的。手术矫正为主要治疗方法，死亡率较低。修复的类型和范围很大程度上取决于狭窄的长度。心脏异常常与之相关，可在气管手术时处理。尽管初始结果令人满意，但由于持续性肉芽组织导致的术后发病率仍很高。通过多学科方法和对修复气道的密切随访，才能为这些病情复杂的患者提供最佳护理。长期生活质量仍不确定。
