Tandon Sandeep, Garg Rajeev Kumar
Government Dental College & Hospital, Department of Pediatric Dentistry, Jaipur, India.
Fetal Pediatr Pathol. 2012 Aug;31(4):195-201. doi: 10.3109/15513815.2011.648719. Epub 2012 Mar 9.
Desmoplastic fibroma (DF) is a benign but locally aggressive tumor usually recognized as an intraosseous counterpart of soft tissue fibromatosis in both gnathic and extra-gnathic sites. The most common site is mandible followed by pelvis and long bones. Maxilla has been reported to be involved very rarely. Desmoplastic fibroma is recently being considered to be one of the oral manifestations of tuberous sclerosis rather than a coincidental finding. We report an unusual case of a girl with a previous diagnosis of tuberosclerosis who presented at 8 years with an oral lesion diagnosed as desmoplastic fibroma.
促结缔组织增生性纤维瘤（DF）是一种良性但具有局部侵袭性的肿瘤，通常被认为是颌骨和颌骨外部位软组织纤维瘤病的骨内对应物。最常见的部位是下颌骨，其次是骨盆和长骨。据报道，上颌骨很少受累。促结缔组织增生性纤维瘤最近被认为是结节性硬化症的口腔表现之一，而不是偶然发现。我们报告了一例不寻常的病例，一名先前被诊断为结节性硬化症的女孩，8岁时出现口腔病变，诊断为促结缔组织增生性纤维瘤。
