Broudy A S, Smith R J
J Hand Surg Am. 1979 Jul;4(4):304-15. doi: 10.1016/s0363-5023(79)80066-0.
Deformities of the hand and wrist in 26 upper limbs of 20 patients with ulnar deficiency were studied. In eight limbs the ulna was totally absent. In the remainder it was severely or moderately hypoplastic. Abnormalities of the digits were present in all affected limbs. There was ectrodactyly in 25 hands. The thumb was hypoplastic in 21 hands and totally absent in five. Digital deformities also included syndactyly (14 hands) and delta phalanx (six hands). Early syndactyly release, pollicization, and rotational osteotomy of the metacarpals improved hand function in many of these patients. In only three of 26 limbs was there more than 20 degrees of fixed ulnar deviation at the wrist. In 16 patients the distal ulnar "anlage" was not removed. None of these patients developed ulnar deviation of the wrist or progressive deformity at the wrist during growth. Resection of the distal ulnar "anlage" does not appear to be warranted, unless there is progressive deformity of the wrist or elbow or increased bowing of the radius.
对20例尺骨发育不全患者的26条上肢的手部和腕部畸形进行了研究。8条上肢尺骨完全缺如。其余上肢尺骨严重或中度发育不全。所有受累上肢均存在手指畸形。25只手有裂手畸形。21只手拇指发育不全，5只手拇指完全缺如。手指畸形还包括并指（14只手）和杵状指（6只手）。早期并指松解、拇指再造和掌骨旋转截骨术改善了许多此类患者的手部功能。26条上肢中只有3条在腕部有超过20度的固定尺骨偏斜。16例患者未切除尺骨远端“原基”。这些患者在生长过程中均未出现腕部尺骨偏斜或腕部进行性畸形。除非存在腕部或肘部进行性畸形或桡骨弯曲增加，否则似乎没有必要切除尺骨远端“原基”。
