Langer M, Grünberger W, Ringler M
1st Department of Obstetrics and Gynecology, Vienna, Austria.
Acta Obstet Gynecol Scand. 1990;69(4):343-9. doi: 10.3109/00016349009036159.
Eleven patients with Mayer-Rokitansky-Küster syndrome (MRK) and 7 patients with adrenogenital syndrome (CVAH) were interviewed and tested pre- and postoperatively. MRK subjects were operated on with a modified Vecchietti procedure, CVAH subjects underwent genitoplastic and clitoroplastic operation. Psychosocial sequelae of and coping with malformation and treatment were assessed with semistructured interviews and the Giessen test. Anatomical and functional results of the vaginoplastic operation were excellent, and sexual satisfaction correlated with coping. 7/11 MRK patients were capable of good to fair adaptation to the malformation, whereas CVAH patients suffered severe distortions of body image. The malformation caused narcissistic damage in all cases. Circumstances of diagnosis, prevailing defense mechanism and consequences for counselling are discussed.
对11例梅耶-罗基坦斯基-库斯特综合征（MRK）患者和7例肾上腺性征异常综合征（CVAH）患者在术前和术后进行了访谈及测试。MRK患者接受了改良韦基耶蒂手术，CVAH患者接受了生殖器整形和阴蒂整形手术。通过半结构化访谈和吉森测试评估了畸形及治疗的心理社会后遗症和应对方式。阴道成形手术的解剖和功能结果良好，性满意度与应对方式相关。11例MRK患者中有7例能够较好地适应畸形，而CVAH患者则遭受了严重的身体形象扭曲。畸形在所有病例中均造成了自恋损伤。讨论了诊断情况、主要防御机制及对咨询的影响。
