Kansu Leyla, Yilmaz Ismail
Department of Otolaryngology Head and Neck Surgery, Baskent University, Ankara, Turkey.
Int J Pediatr Otorhinolaryngol. 2012 Jun;76(6):772-6. doi: 10.1016/j.ijporl.2012.03.003. Epub 2012 Mar 24.
Approximately 10% of patients with peripheral facial nerve palsy are children. Facial nerve palsy is usually idiopathic. An uncommon cause is herpes zoster oticus (Ramsay Hunt syndrome). This syndrome usually affects adults and is rare in children.
We reviewed the literature and describe the cause, clinical manifestations, and treatment of Ramsay Hunt syndrome. We also report a case of the syndrome in a 12-year-old boy.
Ramsay Hunt syndrome is characterized by peripheral facial paralysis associated with herpetic eruption on the auricula and external ear, and by vestibulocochlear dysfunction. It occurs by reactivation of latent varicella-zoster virus (VZV) in the geniculate ganglion, affecting the seventh and eighth cranial nerves. The diagnosis is based on history and physical findings. Treatment of Ramsay Hunt syndrome uses a combination of high-dose corticosteroids and acyclovir. Although the prognosis is better in children than in adults, it is not good enough.
约10%的周围性面神经麻痹患者为儿童。面神经麻痹通常为特发性。一种不常见的病因是耳带状疱疹（拉姆齐·亨特综合征）。该综合征通常影响成人，在儿童中罕见。
我们回顾了文献并描述了拉姆齐·亨特综合征的病因、临床表现及治疗。我们还报告了一名12岁男孩患该综合征的病例。
拉姆齐·亨特综合征的特征为周围性面瘫伴耳廓和外耳道疱疹样皮疹，以及前庭蜗功能障碍。它是由膝状神经节中潜伏的水痘 - 带状疱疹病毒（VZV）重新激活引起的，影响第七和第八对脑神经。诊断基于病史和体格检查结果。拉姆齐·亨特综合征的治疗采用大剂量皮质类固醇和阿昔洛韦联合使用。虽然儿童的预后比成人好，但仍不尽人意。
