Morrow Daniel, Schelonka Robert, Krol Alfons, Davies Michael, Kuang Anna
Division of NeonatologyDepartment of PediatricsDepartment of Pediatric Dermatology, Doernbecher Neonatal Care Center, Oregon Health and Science University, Portland, OregonCasey Eye Institute, Oregon Health and Science University, Portland, OregonDepartment of Pediatric Plastic and Reconstructive Surgery, Oregon Health and Science University, Portland, Oregon.
Pediatr Dermatol. 2013 Nov-Dec;30(6):e208-13. doi: 10.1111/j.1525-1470.2012.01742.x. Epub 2012 Apr 4.
Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co-twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.
先天性皮肤发育不全（ACC）是指先天性皮肤缺失。根据分布情况和相关表现有多种不同的分类。V型ACC的独特之处在于，病变通常是对称的，主要见于躯干，但也可累及上肢和下肢。V型与在孕早期晚期或孕中期早期单卵双胎之一的丢失有关。本文报告1例广泛的V型ACC病例并进行文献复习，包括治疗方法及结果总结。从现有文献来看，早期手术干预并无益处，因此我们提出一种始于保守治疗的治疗方案。
