Jain Deepali, Kohli Kavita
Department of Pathology, Maulana Azad Medical College, New Delhi, India.
Cutis. 2012 Feb;89(2):61-4.
Congenital infantile fibrosarcoma (CIFS) is a rare pediatric soft tissue tumor; clinically, it presents as a highly vascular mass and may simulate a hemangioma. It usually occurs in the first year of life and has a relatively better prognosis compared to other aggressive spindle cell sarcomas of childhood. We report a patient with CIFS who presented with a nonspecific ulcerated mass lesion over the right shoulder region that was clinically diagnosed as a benign vascular lesion. Histology revealed a highly cellular tumor with closely packed fascicles of spindle cells. Immunohistochemically, the tumor cells expressed vimentin.
先天性婴儿纤维肉瘤（CIFS）是一种罕见的儿科软组织肿瘤；临床上，它表现为高度血管化的肿块，可能类似血管瘤。它通常发生在生命的第一年，与儿童期其他侵袭性梭形细胞肉瘤相比，预后相对较好。我们报告一例CIFS患者，其右肩部区域出现非特异性溃疡肿块病变，临床诊断为良性血管病变。组织学检查显示肿瘤细胞高度密集，梭形细胞束紧密排列。免疫组织化学检查显示肿瘤细胞表达波形蛋白。
