Department of Radiology, University Hospitals Leuven, Herestraat 49, 3000 Leuven, Belgium.
Pediatr Radiol. 2012 Sep;42(9):1138-41. doi: 10.1007/s00247-012-2379-1. Epub 2012 Apr 4.
We present a neonate with a complex congenital cardiopathy and a right-sided diaphragmatic hernia complicated with hepatopulmonary fusion. Radiography, abdominal US and multidetector CT (MDCT) demonstrated right-sided lung hypoplasia and liver herniation. In addition, MDCT angiography showed abnormal pulmonary vascular anatomy. At surgery, a right-sided diaphragmatic hernia with a partially herniated liver and hepatopulmonary fusion was confirmed. There was no aberrant systemic vascular supply towards the lower lobe, as seen in extralobar sequestration. MDCT angiography of the chest and upper abdomen with optimal enhancement and reconstruction of the pulmonary and hepatic vasculature can demonstrate associated anomalies in cases of suspected primary or secondary right lung hypoplasia.
我们呈现了一例伴有复杂先天性心脏病和右侧膈疝并伴有肝肺融合的新生儿病例。放射线照相、腹部超声和多排 CT（MDCT）显示右侧肺发育不良和肝脏疝出。此外，MDCT 血管造影显示肺血管解剖异常。手术中，证实存在右侧膈疝，部分肝脏疝出并伴有肝肺融合。与叶外型肺隔离症不同，下叶未见异常体循环血管供应。胸部和上腹部的 MDCT 血管造影，通过优化的肺部和肝脏血管增强和重建，可以在疑似原发性或继发性右肺发育不良的情况下显示相关异常。
