肝肺融合：一种与右先天性膈疝相关的罕见且可能致命的关联。
Hepatopulmonary fusion: a rare and potentially lethal association with right congenital diaphragmatic hernia.
作者信息
Jain Vishesh, Yadav Devendra Kumar, Kandasamy Devasenathipathy, Gupta Devendra Kumar
机构信息
Department of Paediatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
Department of Radiodiagnosis, All India Institute of Medical Sciences, New Delhi, India.
出版信息
BMJ Case Rep. 2017 Feb 14;2017:bcr2016218227. doi: 10.1136/bcr-2016-218227.
Abstract
Hepatopulmonary fusion is an extremely rare accompaniment of right congenital diaphragmatic hernia. It is associated with abnormal systemic arterial supply and venous drainage of the right lung along with congenital heart disease. Children with this condition have a comparatively poor prognosis. We report a case of right congenital diaphragmatic hernia with hepatopulmonary fusion along with review of the literature with stress on diagnosis and management.
摘要
肝肺融合是右先天性膈疝极为罕见的伴随情况。它与右肺异常的体循环动脉供血和静脉引流以及先天性心脏病相关。患有这种病症的儿童预后相对较差。我们报告一例伴有肝肺融合的右先天性膈疝病例，并结合文献复习，重点阐述诊断和治疗。
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3
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4
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9
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10
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