Division of Cardiology, Severance Cardiovascular Hospital, Yonsei University College of Medicine, Seoul, Korea.
Yonsei Med J. 2012 May;53(3):658-61. doi: 10.3349/ymj.2012.53.3.658.
Torsades de pointes is a life-threatening arrhythmia associated with a number of causes, but is very rare among endocrinologic disorders. We report a case of male pseudohermaphroditism with hyperaldosteronism due to a 17α-hydroxylase deficiency presented with sudden cardiac arrest.
尖端扭转型室性心动过速是一种与多种原因相关的危及生命的心律失常,但在内分泌疾病中非常罕见。我们报告了一例因 17α-羟化酶缺乏导致的男性假两性畸形伴醛固酮增多症患者,其表现为心搏骤停。