Izraelit A, Ten V, Krishnamurthy G, Ratner V
Department of Pediatrics, Columbia University College of Physicians and Surgeons, New York, USA.
ISRN Pediatr. 2011;2011:175931. doi: 10.5402/2011/175931. Epub 2010 Dec 29.
Neonatal central cyanosis is always a sign of serious pathological processes and may involve diverse organs and impose a significant diagnostic and therapeutic challenge. Here, we report an unusual presentation of Ebstein's anomaly, a rare congenital heart malformation, as the cause of central cyanosis in a one-week-old full-term infant. Initiation of PEG(1) therapy in neonates with Ebstein's anomaly always needs a very careful consideration because of a high risk for the development of a "circular shunt" leading to severe deterioration of multiple organs perfusion.
新生儿中枢性发绀始终是严重病理过程的一种表现,可能累及多个器官,带来重大的诊断和治疗挑战。在此,我们报告1例1周龄足月儿因罕见的先天性心脏畸形——埃布斯坦畸形(Ebstein's anomaly)导致中枢性发绀的不寻常病例。由于存在发生“环状分流”导致多器官灌注严重恶化的高风险,因此对患有埃布斯坦畸形的新生儿启动聚乙二醇(PEG)治疗时始终需要非常谨慎地考虑。