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落叶型天疱疮

Pemphigus foliaceus.

作者信息

Fariba Ghalamkarpour, Ayatollahi Azin, Hejazi Somayeh

机构信息

Shahid Beheshti University Shohada-e Tajrish Hospital, Tehran, Iran.

出版信息

Indian Pediatr. 2012 Mar;49(3):240-1.

Abstract

Pemphigus foliaceus is an autoimmune blistering disease, which affects the skin but rarely affects the mucosae. There are two variants of pemphigus foliaceus : endemic and sporadic. Erythroderma due to pemphigus foliaceus is unusual and its occurrence in a child is very rare. We describe a case of erythrodermic pemphigus foliaceus in a 12- year- old boy.

摘要

落叶型天疱疮是一种自身免疫性水疱病,主要累及皮肤,很少累及黏膜。落叶型天疱疮有两种类型:地方性和散发性。由落叶型天疱疮引起的红皮病并不常见,在儿童中发生则极为罕见。我们报告一例12岁男孩患红皮病型落叶型天疱疮的病例。

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