Ding Ying, Zhang Hong, Song Guo-xiang
Department of Ophthalmology, the Second Hospital of Tianjin Medical University, Tianjin 300211, China.
Zhonghua Yan Ke Za Zhi. 2012 Jan;48(1):47-51.
To conclusion the clinical features and image features, the diagnosis and management of orbital hemangiopericytoma, in order to direct clinical diagnosis and differential diagnosis.
Seventeen patients with pathologically confirmed orbital hemangiopericytoma were analyzed retrospectively.
Patients usually complained of exophthalmos. Fourteen patients can be touched the tumor in the orbit. In B-scan ultrasound, a well outlined lesion was revealed. The type of it was often similarly circular or anomaly. The extent of internal echo was associated with histological structure of lesion. Color doppler flow imaging show that the tumor has rich feeding vessels. Some of them is arterial feeding vessels. On CT scan, hemangiopericytoma generally appears to be a uniform high-density mass with obvious enhancement upon injection of contrast material. All cases underwent surgical resection and are proved by pathological examination.
Orbital hemangiopericytoma is a potentially malignant tumor. The prognosis and clinical behavior can't be predicted on the basis of their histopathologic classification. Medical imaging can help to demonstrate the site, configuration, and characteristics of the tumors and contribute to the treatment. But, there has not characteristic medical features. The final diagnosis must be depend on the pathology. The best management of hemangiopericytoma is complete local excision. All the patients must be observed nearly.
总结眼眶血管外皮瘤的临床特征、影像特征、诊断及治疗方法，以指导临床诊断与鉴别诊断。
回顾性分析17例经病理确诊的眼眶血管外皮瘤患者。
患者常主诉眼球突出。14例可于眼眶内触及肿物。B超显示肿物边界清晰，形态多呈类圆形或不规则形，内部回声情况与肿物组织结构有关。彩色多普勒血流成像显示肿瘤供血丰富，部分有动脉供血。CT扫描显示血管外皮瘤通常表现为均匀高密度肿块，增强扫描后强化明显。所有病例均行手术切除，术后经病理证实。
眼眶血管外皮瘤是一种潜在恶性肿瘤，其预后和临床行为不能依据组织病理学分类预测。医学影像有助于显示肿瘤的部位、形态及特征，对治疗有帮助，但无特征性影像表现。最终诊断必须依靠病理。血管外皮瘤的最佳治疗方法是完整局部切除。所有患者均需密切随访。
