Haddad Élie, Barnes David, Kafal Ayman
CHU Sainte-Justine, 3175 Cote Sainte-Catherine, Montreal, QC, Canada H3T 1C5.
Transfus Apher Sci. 2012 Jun;46(3):315-21. doi: 10.1016/j.transci.2012.03.022. Epub 2012 Apr 12.
The most frequently encountered patients with primary immunodeficiency disease (PID) are those with antibody deficiencies. These patients require life-long immunoglobulin (IgG) replacement therapy to prevent severe and reoccurring infections. IgG is traditionally administered intravenously (IVIG) on an outpatient basis, although in some Scandinavian countries subcutaneous administration of IgG (SCIG) as home self-infusion has become the predominant mode of delivery. Compared with IVIG, SCIG therapy leads to a more physiologic IgG profile since the large variations between peak and trough levels of serum IgG are blunted by slow absorption and maintenance of closer equilibrium between intra- and extravascular compartments. SCIG therapy has been shown to be as effective as IVIG in preventing infections and has a better safety profile, with fewer systemic side effects. While local tissue reactions are common with SCIG, they are usually mild, tend to improve over time and typically do not interfere with therapy. Switching to SCIG therapy from IVIG can lead to significant improvements in health-related quality of life, appears to be more convenient for the patient, and can make it easier for the patient to travel. In those patients with difficult vascular access and intolerable side-effects with IVIG therapy, SCIG therapy may be the only treatment option. Selected patients can be expected to benefit greatly from SCIG therapy, although implementation of a successful home-treatment program requires proper education, training, and supportive care.
原发性免疫缺陷病(PID)患者中最常见的是抗体缺陷患者。这些患者需要终身接受免疫球蛋白(IgG)替代疗法,以预防严重和反复感染。传统上,IgG是在门诊静脉注射(IVIG),不过在一些斯堪的纳维亚国家,皮下注射IgG(SCIG)进行家庭自我输注已成为主要的给药方式。与IVIG相比,SCIG疗法可使IgG水平更接近生理状态,因为血清IgG峰值和谷值之间的巨大差异会因吸收缓慢以及血管内和血管外 compartments之间维持更紧密的平衡而变得平缓。已证明SCIG疗法在预防感染方面与IVIG一样有效,且安全性更好,全身副作用更少。虽然SCIG治疗时局部组织反应很常见,但通常较轻,会随着时间推移而改善,并且一般不会干扰治疗。从IVIG转换为SCIG疗法可显著改善健康相关生活质量,对患者来说似乎更方便,还能使患者出行更容易。对于那些血管通路困难且IVIG治疗有无法耐受的副作用的患者,SCIG疗法可能是唯一的治疗选择。部分患者有望从SCIG疗法中大大受益,不过要实施成功的家庭治疗方案,需要进行适当的教育、培训和支持性护理。