Corno F, Pera A, Toppino M, Panier Suffat P, Tridico F, Rovere V, Iozzia C, Contessa L, Zan S
Istituto di Clinica Chirurgica Generale e Terapia Chirurgica, Università degli Studi di Torino.
Minerva Chir. 1990 Jun 30;45(12):895-8.
The paper reports a case of mesenteric fibromatosis with familial polyposis, an association which was diagnosed as Gardner's syndrome, and highlights the complications connected to mesenterial desmoid tumours. In addition, the importance of radical surgical therapy of these neoplasias is underlined. Lastly, it is hypothesised that full screening of patients affected by familial polyposis might show a greater incidence of association between widespread polyposis and pathological changes attributable to Gardner's syndrome.
本文报道了一例伴有家族性息肉病的肠系膜纤维瘤病,这种关联被诊断为加德纳综合征,并强调了与肠系膜硬纤维瘤相关的并发症。此外,还强调了对这些肿瘤进行根治性手术治疗的重要性。最后,推测对家族性息肉病患者进行全面筛查可能会发现广泛息肉病与加德纳综合征所致病理变化之间的关联发生率更高。