Roscher R, Gaedicke G, Mohr W
Klinik für Allgemeinchirurgie, Universität Ulm.
Monatsschr Kinderheilkd. 1988 Jul;136(7):393-6.
A case of omento-mesenterial fibromatosis in a 6-year-old boy revealing through acute intestinal obstruction is reported. Mesenterial fibromatosis, also known as aggressive fibromatosis or desmoid tumor is generally associated with Gardner's syndrome but otherwise an extremely rare disease. Fibromatoses do not metastasize but are characterized by a high incidence of local recurrence. Primary treatment is operative. After multiple recurrence irradiation, cytostatics and antiestrogens have been used additionally to control the disease.
报告了一例6岁男孩网膜肠系膜纤维瘤病,通过急性肠梗阻发现。肠系膜纤维瘤病,也称为侵袭性纤维瘤病或硬纤维瘤,通常与加德纳综合征相关,但除此之外是一种极其罕见的疾病。纤维瘤病不发生转移,但具有局部复发率高的特点。主要治疗方法是手术。在多次复发后,已额外使用放疗、细胞抑制剂和抗雌激素来控制病情。